Hemophilia results from mutations at the factor VIII or IX loci on the X chromosome and each occurs in mild, moderate, and severe forms. Show
What is Hemophilia?Hemophilia is now on the rise among the pediatric population across the world.
PathophysiologyPathophysiologies for both hemophilia A and B are as follows: Hemophilia A
Hemophilia B
Statistics and IncidencesHemophilia is slowly progressing among pediatric patients in all parts of the globe.
CausesThe causes of both hemophilia A and B are apparently from a genetic form.
Clinical ManifestationsHemophilia is suggested by a history of hemorrhage disproportionate to trauma or of spontaneous hemorrhage, or a family history of bleeding problems.
Assessment and Diagnostic FindingsThe diagnosis of hemophilia A and B is established by measuring the following:
Medical ManagementThe treatment of hemophilia may involve prophylaxis, management of bleeding episodes, treatment of factor VIII (FVIII) inhibitors, and treatment and rehabilitation of hemophilia synovitis.
Pharmacologic ManagementMedications of choice for patients with hemophilia are:
Nursing ManagementNursing care for a child with hemophilia include: Nursing AssessmentAssessment in a child with hemophilia include the following:
Nursing DiagnosesBased on the assessment data, the major nursing diagnoses are:
Nursing Care Planning and GoalsMain Article 5 Hemophilia Nursing Care Plans The major goals are:
Nursing InterventionsThe nursing interventions for a child with hemophilia are:
EvaluationGoals are met as evidenced by:
Documentation GuidelinesDocumentation in a child with hemophilia include the following:
Practice Quiz: HemophiliaHere’s a 5-item quiz for Hemophilia study guide. Please visit our nursing test bank page for more NCLEX practice questions. 1. Mr. and Mrs. Smith’s child has hemophilia; which of the following actions would you instruct them to avoid? A. Lowering the injured area. 1. Answer: A. Lowering the injured area.
2. Which of the following laboratory tests is most effective in diagnosing hemophilia? A. Complete blood count (CBC). 2. Answer: D. Partial thromboplastin time (PTT).
3. A child with known hemophilia A was brought to the emergency room with complaints of nose bleeding and some bruises in the joints. Which of the following should the nurse anticipate to be given to the child? A. Cyclosporine. 3. Answer: C. Factor VIII.
4. The mother of a child with hemophilia asks the nurse which over-the-counter medication is suitable for her child’s joint discomfort. The nurse should tell the mother to purchase: A. Aspirin (Acetylsalicylic acid). 4. Answer: C. Tylenol (acetaminophen).
5. Which of the following disorders results from a deficiency of factor VIII? A. Sickle cell disease. 5. Answer: C. Hemophilia A.
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